dc.creator | López Ruiz, José Antonio | es |
dc.creator | Tallón Aguilar, Luis | es |
dc.creator | Sánchez Moreno, Laura | es |
dc.creator | López Pérez, José | es |
dc.creator | Pareja Ciuró, Felipe | es |
dc.creator | Oliva Mompean, Fernando | es |
dc.creator | Padillo Ruiz, Francisco Javier | es |
dc.date.accessioned | 2024-05-23T12:39:19Z | |
dc.date.available | 2024-05-23T12:39:19Z | |
dc.date.issued | 2016 | |
dc.identifier.citation | López Ruiz, J.A., Tallón Aguilar, L., Sánchez Moreno, L., López Pérez, J., Pareja Ciuró, F., Oliva Mompean, F. y Padillo Ruiz, F.J. (2016). Hirschsprung disease with debut in adult age as acute intestinal obstruction: case report. Revista Española de Enfermedades Digestivas, 108 (11), 742-745. https://doi.org/10.17235/reed.2016.3841/2015. | |
dc.identifier.issn | 1130-0108 | es |
dc.identifier.issn | 2340-4167 | es |
dc.identifier.uri | https://hdl.handle.net/11441/158887 | |
dc.description.abstract | Hirschsprung’s disease is characterized by absence of ganglion
cells in submucosal and myenteric plexus of distal bowel. Most cases
become manifest during the neonatal period, but in rare instances,
this disease is initially diagnosed in adult age. It usually presents as
severe constipation with colonic dilatation proximal to the agangli
onic segment. The treatment is surgical, removing the aganglionic
segment and restoring continuity of digestive tract. The disease
rarely presents as an acute intestinal obstruction. We report a case
not previously diagnosed, which presented as a massive colonic
dilatation with a maximum diameter of 44 cm, with imminent risk
of drilling that forced to perform an emergency surgery. We include
a review of existing literature. | es |
dc.format | application/pdf | es |
dc.format.extent | 4 p. | es |
dc.language.iso | eng | es |
dc.publisher | Aran Ediciones S.A. | es |
dc.relation.ispartof | Revista Española de Enfermedades Digestivas, 108 (11), 742-745. | |
dc.rights | Attribution-NonCommercial-NoDerivatives 4.0 Internacional | * |
dc.rights.uri | http://creativecommons.org/licenses/by-nc-nd/4.0/ | * |
dc.subject | Hirschsprung disease | es |
dc.subject | Megacolon | es |
dc.subject | Intestinal obstruction | es |
dc.title | Hirschsprung disease with debut in adult age as acute intestinal obstruction: case report | es |
dc.type | info:eu-repo/semantics/article | es |
dc.type.version | info:eu-repo/semantics/publishedVersion | es |
dc.rights.accessRights | info:eu-repo/semantics/openAccess | es |
dc.contributor.affiliation | Universidad de Sevilla. Departamento de Cirugía | es |
dc.relation.publisherversion | https://www.reed.es/ArticuloFicha.aspx?id=647&hst=0&idR=42&tp=1 | es |
dc.identifier.doi | 10.17235/reed.2016.3841/2015 | es |
dc.journaltitle | Revista Española de Enfermedades Digestivas | es |
dc.publication.volumen | 108 | es |
dc.publication.issue | 11 | es |
dc.publication.initialPage | 742 | es |
dc.publication.endPage | 745 | es |