Article
Hirschsprung disease with debut in adult age as acute intestinal obstruction: case report
Author/s | López Ruiz, José Antonio
Tallón Aguilar, Luis Sánchez Moreno, Laura López Pérez, José Pareja Ciuró, Felipe Oliva Mompean, Fernando Padillo Ruiz, Francisco Javier |
Department | Universidad de Sevilla. Departamento de Cirugía |
Publication Date | 2016 |
Deposit Date | 2024-05-23 |
Published in |
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Abstract | Hirschsprung’s disease is characterized by absence of ganglion
cells in submucosal and myenteric plexus of distal bowel. Most cases
become manifest during the neonatal period, but in rare instances,
this disease is ... Hirschsprung’s disease is characterized by absence of ganglion cells in submucosal and myenteric plexus of distal bowel. Most cases become manifest during the neonatal period, but in rare instances, this disease is initially diagnosed in adult age. It usually presents as severe constipation with colonic dilatation proximal to the agangli onic segment. The treatment is surgical, removing the aganglionic segment and restoring continuity of digestive tract. The disease rarely presents as an acute intestinal obstruction. We report a case not previously diagnosed, which presented as a massive colonic dilatation with a maximum diameter of 44 cm, with imminent risk of drilling that forced to perform an emergency surgery. We include a review of existing literature. |
Citation | López Ruiz, J.A., Tallón Aguilar, L., Sánchez Moreno, L., López Pérez, J., Pareja Ciuró, F., Oliva Mompean, F. y Padillo Ruiz, F.J. (2016). Hirschsprung disease with debut in adult age as acute intestinal obstruction: case report. Revista Española de Enfermedades Digestivas, 108 (11), 742-745. https://doi.org/10.17235/reed.2016.3841/2015. |
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