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      Genetic Rescue of Mitochondrial and Skeletal Muscle Impairment in an Induced Pluripotent Stem Cells Model of Coenzyme Q10 Deficiency 

      Romero Moya, Damià; Santos Ocaña, Carlos; Castaño, Julio; Garrabou, Gloria; Rodríguez Gómez, José Antonio; Ruiz Bonilla, Vanesa; Bueno, Clara; González Rodríguez, Patricia; Giorgetti, Alessandra; Perdiguero, Eusebio; Prieto, Cristina; Moren Núñez, Constanza; Fernández Ayala, Daniel J.; Victoria Cascajo, María; Velasco, Iván; Canals, Josep María; Montero, Raquel; Yubero, Delia; Jou, Cristina; López Barneo, José; Cardellac, Francesc; Muñoz Cánoves, Pura; Artuch, Rafael; Navas, Plácido; Menéndez, Pablo (Wiley-Blackwell, 2017-07)
      Coenzyme Q10 (CoQ10) plays a crucial role in mitochondria as an electron carrier within the mitochondrial respiratory chain ...