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Listar por autor "Aguilar Moncayo, Matilde"
Mostrando ítems 1-6 de 6
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Artículo
A Bicyclic 1-Deoxygalactonojirimycin Derivative as a Novel Pharmacological Chaperone for GM1 Gangliosidosis
Takai, Tomoko; Higaki, Katsumi; Aguilar Moncayo, Matilde; Mena Barragán, Teresa; Hirano, Yuki; Yura, Kei; García Moreno, M. Isabel; Ortiz Mellet, Carmen; García Fernández, José Manuel; Suzuki, Yoshiyuki (Cell Press, 2013)Lysosomal β-galactosidase (β-Gal) deficiency causes a group of disorders that include neuronopathic GM1 gangliosidosis and ...
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Artículo
Bicyclic (galacto)nojirimycin analogues as glycosidase inhibitors: Effect of structural modifications in their pharmacological chaperone potential towards β-glucocerebrosidase
Aguilar Moncayo, Matilde; García Moreno, M. Isabel; Trapero, Ana; Egido Gabás, Meritxell; Llebaria, Amadeu; García Fernández, José Manuel; Ortiz Mellet, Carmen (Royal Society of Chemistry (Great Britain), 2011)A molecular-diversity-oriented approach for the preparation of bicyclic sp2-iminosugar glycomimetics related to nojirimycin ...
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Patente. Invención
Compuestos potenciadores de la actividad de glicosidasas mutantes
García Fernández, José Manuel; Ortiz Mellet, Carmen; García Moreno, María Isabel; Aguilar Moncayo, Matilde; Suzuki, Yoshiyuki; Ohno, Kousaku (Oficina Española de Patentes y Marcas (OEPM), 2011-01-13)Compuestos potenciadores de la actividad de glicosida sas mutantes, con actividad inhibidoras de enzimas gli cosidasas y ...
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Artículo
Cyclodextrin-mediated Crystallization of Acid β-glucosidase in Complex with Amphiphilic Bicyclic Nojirimycin Analogues
Brumshtein, Boris; Aguilar Moncayo, Matilde; Benito, Juan Manuel; García Fernández, José Manuel; Silman, Israel; Shaaltiel, Yoseph; Aviezer, David; Sussman, Joel L.; Futerman, Anthony H.; Ortiz Mellet, Carmen (Royal Society of Chemistry, 2011)Cyclodextrin-based host-guest chemistry has been exploited to facilitate co-crystallization of recombinant human acid ...
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Artículo
Hydrothermal preparation of highly photoactive TiO2 nanoparticles
Hidalgo López, María del Carmen; Maicu, Marina; Navío Santos, José Antonio; Colón Ibáñez, Gerardo; Aguilar Moncayo, Matilde (Elsevier, 2007)TiO2 nanoparticles have been prepared by amine assisted sol–gel precipitation of Ti4+ aqueous solutions and further ...
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Artículo
Structural basis of pharmacological chaperoning for human β-galactosidase
Suzuki, Hironori; Ohto, Umeharu; Higaki, Katsumi; Mena Barragán, Teresa; Aguilar Moncayo, Matilde; Ortiz Mellet, Carmen; Nanba, Eiji; García Fernández, José Manuel; Suzuki, Yoshiyuki; Shimizu, Toshiyuki (Elsevier, 2014)GM1 gangliosidosis and Morquio B disease are autosomal recessive diseases caused by the defect in the lysosomal β-galactosidase ...